Arrhythmogenic Right Ventricular Dysplasia: a case report and review of the literature

A. Rbaibi , M. Chtioui .
Page No 34-41

Arrhythmogenic right ventricular dysplasia (ARVD) is a right ventricular cardiomyopathy
characterized by partial or total replacement of normal myocardium by fatty or fibrofatty tissue.
This disease affects the right ventricle. The left ventricle is rarely involved. The exact prevalence is
unknown. It represents, after hypertrophic cardiomyopathy, the leading cause of sudden cardiac
death in young patients, especially athletes. She has a male predominance. Sudden death by
ventricular tachycardia or ventricular fibrillation can be the inaugural event. The diagnostic
criteria developed in 2010 are very useful in the diagnosis of ARVD, especially in mild forms. The
three imaging cited, and therefore useful diagnostic modalities are echocardiography, magnetic
resonance imaging (MRI) and conventional angiography RV. The therapeutic management of
patients with ARVD is based on antiarrhythmics especially beta-blockers and catheter ablation.
Implantable cardioverter defibrillator ICD may be indicated for primary or secondary prevention
of sudden death and improves the survival of patients with ARVD at high risk.